ICD-9 Codes for Diseases and Disorders Related to Dementia

Annotated List of ICD-9-CM Codes for Diseases and Disorders Related to Dementia. The Primary and Secondary codes are to be listed in Section I Item 3 a (and b if secondary code is listed) when reporting to the Alzheimer's and other Dementia Registry as part of completing Section S Item 4 i. This list of codes was compiled 10/30/97, edited 4/01/2000, 11/08/2007.
 Primary   Secondary  Diagnosis
042 290.1 HIV/Presenile Dementia
042 294.9 HIV/Unspecified Organic Brain Syndrome
042 298.9 HIV/Unspecified Psychosis
042 310.9 HIV/Organic Dementia
046.0   Kuru
046   Slow Virus Infection of Central Nervous System
046.1   Jakob-Creutzfeldt Disease
046.2   Subacute Sclerosing Panencephalitis
046.3   Progressive Multifocal Leukoencephalopathy
094   Neurosyphilis
094.1   General Paresis
290   Senile and Presenile Organic Psychotic Conditions
290.0   Senile Dementia, Uncomplicated
290.1 046.1 Presenile Dementia/Jakob-Creutzfeldt Disease
290.1 331.0 Presenile Dementia/Alzheimer's Disease
290.1 331.1 Presenile Dementia/Pick's Disease
290.10   Presenile Dementia, Uncomplicated
290.11   Presenile Dementia with Delirium
290.12   Presenile Dementia with Delusion or Binswanger's Disease
290.13   Presenile Dementia with Depression
290.20   Senile Dementia with Delusion
290.2   Senile Dementia, with Delusional or Depressive Features
290.21   Senile Dementia with Depression
290.3   Senile Dementia with Delirium
290.4 437.0 Arteriosclerotic Dementia(Multi-Infarct)/Cerebral Atherosclerosis
290.4   Arteriosclerotic Dementia (Multi-infarct)
290.40   Arteriosclerotic Dementia Uncomplicated
290.41   Arteriosclerotic Dementia with Delirium
290.42   Arteriosclerotic Dementia with Delusion
290.43   Arteriosclerotic Dementia with Depression
290.8   Other Senile/presenile Organic Psychotic Conditions
290.9   Unspecified Senile Psychotic Condition
291   Alcoholic Psychoses
291.1   Korsakoff's Psychosis, Alcoholic
291.2   Other Alcoholic Dementia
292.82   Drug-Induced Dementia
294.0   Korsakoff's Psychosis, (Non-Alcoholic)
294   Other Organic Psychotic Conditions (Chronic)
294.1 094.1 Dementia in Other Specified Conditions/General Paresis
294.1 275.1 Dementia in Other Specified Conditions/Hepatolenticular Degeneration
294.1 330.1 Dementia in Other Specified Conditions/Cerebral Lipidosis
294.1 340 Dementia in Other Specified Conditions/Multiple Sclerosis
294.1 446.0 Dementia in Other Specified Conditions/Polyarteritis Nodosa
294.1 345.0 -345.9 Dementia in Other Specified Conditions/Epilepsy
294.8 345.0 -345.9 Other Specified Organic Brain Syndromes (Chronic)/Epileptic Psychosis
294.8   Other Specified Organic Brain Syndromes (Chronic)
294.9   Unspecified Organic Brain Syndrome (Chronic)
298.9   Unspecified Psychosis
310   Specific Nonpsychotic Mental Disorders Due to Organic Brain Damage
310.1   Organic Personality Syndrome
310.8   Other Specified Nonpsychotic Mental Disorders, Following Organic Brain Damage
310.9   Unspecified Nonpsychotic Organic Brain Damage
331.0   Alzheimer's Disease
331   Other Cerebral Degenerations
331.1   Pick's Disease
331.2   Senile Degeneration of the Brain
331.3   Communicating Hydrocephalus
331.7 265.0 Cerebral Degeneration in Diseases Classified Elsewhere/Thiamine Deficiency
331.7 266.2 Cerebral Degeneration in Diseases Classified Elsewhere/Vitamin B12 (Folate) Deficiency
331.7 140-239.9 Cerebral Degeneration in Diseases Classified Elsewhere/Neoplastic Disease
331.7 244.0-244.9 Cerebral Degeneration in Diseases Classified Elsewhere/Myxedema (Hypo-and Hyperthyroidism)
331.7 303.0-303.9 Cerebral Degeneration in Diseases Classified Elsewhere/Alcoholism
331.7 430-438 Cerebral Degeneration in Diseases Classified Elsewhere/Cerebrovascular Disease
331.7 741.0,742.3 Cerebral Degeneration in Diseases Classified Elsewhere/Congenital Hydrocephalus
331.8   Other Cerebral Degeneration
331.82   Dementia with Lewy Bodies
331.89   Other Cerebral Degeneration (NEC) (Cerebral Ataxia)
331.9   Cerebral Degeneration, Unspecified
332.0   Paralysis Agitans
332   Parkinson's Disease
333.4   Huntington's Chorea
437.0   Cerebral Atherosclerosis
437   Other and Ill-Defined Cerebrovascular Disease
797   Senility Without Mention of Psychosis